Aplasia of the right lung and calcifying epithelioma in association with Goldenhar's syndrome.

نویسندگان

  • M M Kenawi
  • J A Dickson
چکیده

Case report An 81-year-old male was brought to the Casualty Department, Kingston Public Hospital, Jamaica, and was pronounced dead on arrival. According to the relative, the main complaint of the deceased had been, for some time, recurrent abdominal pain and loss of weight. External examination revealed the deceased to be moderately built and emaciated. There was no clubbing of the fingers or evidence of external injury or violence. There was marked cyanosis. Internal examination showed the lungs to be congested and oedematous and there were signs of chronic bronchitis with emphysema. The pericardium and mediastinal glands were normal. The heart weighed 300 g and the valves were healthy. The coronary arteries were patent but showed arteriosclerotic changes. Marked arteriosclerotic changes were also seen in all the major blood-vessels. There was a bulging mass, yellowish white in colour, in the upper end of the anterior wall of the left ventricle (nearer to the mitral valve). It was a non-polypoid mass measuring 2 x 1 5 x 1 cm and growing from the myocardium and partially filling the left ventricular cavity. The base of the tumour involved the anterior wall of the left ventricle. Microscopically, HE-stained sections showed a fairly cellular tumour extensively infiltrating the heart muscle. The cells were arranged diffusely in some areas and in others were separated by connective tissue septa giving an alveolar pattern. The tumour cells irregularly lined the 'alveoli' with some cells lying free in the lumina (Fig. 1). The cells were round with abundant eosinophilic cytoplasm and

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عنوان ژورنال:
  • Postgraduate medical journal

دوره 52 607  شماره 

صفحات  -

تاریخ انتشار 1976